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Research Article | Open Access
Volume 3 | Issue 9 | Year 2016 | Article Id. IJMS-V3I9P101 | DOI : https://doi.org/10.14445/23939117/IJMS-V3I9P101

Moya Moya Disease - A Rare Case of Cerebro Vascular Disease

Vinjam Brahma Naidu, Valiveti. Pavan Datta Syam Kumar, Bandarupalli Tharun and Dr.N.V. Sundara Chary

Citation :

Vinjam Brahma Naidu, Valiveti. Pavan Datta Syam Kumar, Bandarupalli Tharun and Dr.N.V. Sundara Chary, "Moya Moya Disease - A Rare Case of Cerebro Vascular Disease," International Journal of Medical Science, vol. 3, no. 9, pp. 1-4, 2016. Crossref, https://doi.org/10.14445/23939117/IJMS-V3I9P101

Abstract

Moya Moya Disease [1,3] is a chronic progressive non atherosclerotic non inflammatory non amyloid occlusive intracranial vasculopathy of unknown cause. Incidence is 1 per 1,00,000 In our case, 15 months baby presented with history of seizures, 3-4 events per month followed by paucity of right sided movements. CT Brain showed large areas of post ictal edema in the left fronto - parietal lobes and gliotic areas in the right parieto – occipital lobes. MR Angiogram with Right Carotid injection showed supraclinoid occlusion with collaterals and Vertebro Basillar injection showed multiple collaterals giving Puff of Smoke [2] appearance which is diagnostic of Moya Moya Disesae. Child was treated surgically by Encephalo Myo Synangiosis [4] (EMS).

Keywords

Moya Moya Disease, MR Angiogram, Puff of Smoke, Encephalo Myos Synangiosis.

References

[1] R. Michael Scott, M.D., and Edward R. Smith, M.D - .Moyamoya Disease and Moyamoya Syndrome – New England Journal of Medicine :  May 13, 2009
[2] Suzuki J, Takaku A. Cerebrovascular “moyamoya” disease: disease showing abnormal net-like vessels in base of brain. Arch Neurol 1969;20:288-99.
[3] Moya Moya Disease - www.socialstyrelsen.se/rarediseases - August 23,2014
[4] Surgical Management of Moyamoya Disease by Steven D. Chang, M.D., And Gary K. Steinberg, M.D., Ph.D., Stanford University, U.S.A.